Jorge Martínez-Cedillo, Department of Medical Oncology, Instituto Nacional de Cancerología, Mexico City, Mexico
Rossio Medina-Barrionuevo, Medical Oncology Resident, Instituto Nacional de Cancerología, Mexico City, Mexico
Gregorio Chanona-Vilchis, Department of Pathology, Instituto Nacional de Cancerología, Mexico City, Mexico
Desmoplastic small round blue cell tumor is a rare neoplasm of the mesenchymal tissue. It occurs in adolescents and young adults with a median age of 22 years. Characteristically, it affects the intra-abdominal area, although other locations, including the paratesticular area, have been described in recent years. Usually, it has an aggressive clinical evolution with multiple recurrences, invasion to adjacent structures, and distant metastasis. Case presentation: We report the case of a 23-year-old male with symptoms of pain and testicular volume enlargement who underwent radical right orchiectomy with pathology report of desmoplastic small round blue cell tumor. He received intravenous chemotherapy with the vincristine, Adriamycin, cyclophosphamide/ifosfamide and etoposide regimen for 17 courses, with subsequent recurrence at the inguinal and retroperitoneal level, and surgery plus postoperative radiotherapy was therefore carried out. At the conclusion of radiotherapy, he progressed at the systemic, pulmonary, and hepatic levels and died due to multiple organ failure.
Keywords: Paratesticular desmoplastic tumor. Multimodal treatment.
